Concentration Details

Metabolite
HMDB0061189 (3-Hydroxyisovalerylcarnitine)
Biospecimen
Blood
Status
Detected and Quantified
Data source
Referenced
Concentration
4.81 +/- 0.47 uM
Age
Children (1 - 13 years old)
Sex
Not Specified
Condition
3-hydroxy-3-methylglutaric aciduria
References
    1. Dos Santos Mello M, Ribas GS, Wayhs CA, Hammerschmidt T, Guerreiro GB, Favenzani JL, Sitta A, de Moura Coelho D, Wajner M, Vargas CR: Increased oxidative stress in patients with 3-hydroxy-3-methylglutaric aciduria. Mol Cell Biochem. 2015 Apr;402(1-2):149-55. doi: 10.1007/s11010-014-2322-x. Epub 2015 Jan 4. [PubMed:25557019 ]